Key Points • Idiopathic pulmonary fibrosis (IPF) is a fatal, progressive, scarring lung disease with a variable course. • The goals of palliative care are to provide symptom management, prevent and relieve suffering, and support the best possible quality of life, regardless of stage of the disease or need for other therapies.
Idiopathic pulmonary fibrosis (IPF) is a fatal, progressive, scarring lung disease with a variable course. 1 Mean survival from diagnosis ranges from 2 to 3 years, with some patients dying within the first year following diagnosis. 2,3 Management of patients with IPF is particularly challenging because there is no medical therapy with proven survival benefit.
Palliative care is not the same as end-of-life care. Palliative care focuses on improving or maintaining quality of life through symptom relief, assessing tolerance for curative treatment and easing transitions when curative treatment is no longer an option. Palliative care incorporates the hopes and values of patients and their family members.
Background: Idiopathic pulmonary fibrosis (IPF) is a progressive disease with median survival from 2 to 7 years. Palliative care is an important part of patients´ care as lung transplantation is not an option for the majority of patients. The aim of this study was to describe treatment practices, decision-making and symptoms during end-of-life
Background: Idiopathic Pulmonary Fibrosis has 3 year mean survival with many unmet palliative care needs (Bajwah et al , Lung 2012). Method: 2 year review of in-patient Pulmonary Fibrosis (PF) deaths. Results: 30 patients, 73% male, mean age at death 72.1(42-91). ![Figure] 4(13%) diagnosed PF during final admission. Remaining 24/26 known to Chest team.
I recall a middle-aged man with end-stage pulmonary fibrosis who described to me his pain as if he was always drowning. Despite chronic oxygen therapy, anxiolytics, and opiates, we could not get him to feel better — and the sensation of drowning was torture. He was miserable and we were horrified that we could not help him.
The drugs are in place and regimes agreed upon that will hold me secure through the difficult days leading to those final moments.” – David, who was in the final stages of idiopathic pulmonary fibrosis We consulted with patients and carers, who reported that breathlessness can be a particularly distressing symptom towards the end of life.
Palliative care and hospice appear to be underused in patients with advanced diseases other than cancer. Because the only curative option for some end-stage restrictive lung diseases is lung transplantation, if transplantation is not an option, palliation of symptoms and hospice care may offer patients and families the opportunity to die with ...
Pulmonary fibrosis (scarring throughout the lungs) symptoms are shortness of breath, coughing, and diminished exercise tolerance. Idiopathic pulmonary fibrosis describes a condition in which the cause is unknown. Pulmonary fibrosis has many causes such as exposure to asbestos, infections, lupus, RA, and medication.
Several signs and symptoms indicate that a patient is medically appropriate for hospice care. In general, hospice patients are thought to have six months or less to live if a disease takes its naturals course. Only a doctor can make a clinical determination of life expectancy. However, look for these signs that the disease has progressed …